Self-healing Langerhans cell histiocytosis (Hashimoto-Pritzker disease): two Tunisian cases.
نویسندگان
چکیده
Self-healing Langerhans cell histiocytosis (SHLCH) is a rare self-limited variant of Langerhans cell histiocytosis that presents at birth or during the neonatal period. It was first described by Hashimoto and Pritzker in 1973. Subsequently, more than 70 cases have been reported in the literature. Regarding age of onset, SHLCH should be divided into congenital SHLCH and rare late-onset type. We report here two additional cases of SHLCH in Tunisian infants. We emphasize the need for long-term follow-up in such patients.
منابع مشابه
Solitary, late-onset, self-healing Langerhans cell histiocytosis.
© 2011 The Authors. doi: 10.2340/00015555-0990 Journal Compilation © 2011 Acta Dermato-Venereologica. ISSN 0001-5555 “Self-healing” Langerhans’ cell histiocytosis (LCH), first reported by Hashimoto & Pritzker in 1973 (1), is a rare primary skin disorder that presents at birth or just after birth. It can be categorized based on the involvement of solitary or multiple sites and can be further cla...
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متن کامل[Disseminated crusted papules in a newborn].
BACKGROUND Congenital self-healing Langerhans cell histiocytosis (Hashimoto-Pritzker disease) is the rarest form of Langerhans cell histiocytosis, usually confined to the skin and/or mucous membranes. Cutaneous eruption is mostly generalized, papular, nodular or vesicular. Despite impressive clinical presentation in a newborn it infrequently spreads to internal organs (which then portends a gra...
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Congenital self-healing reticulohistiocytosis, also known as Hashimoto-Pritzker disease, is a single system Langerhans cell histiocytosis that typically presents in healthy newborns and spontaneously regresses. In the present report, we described a 2-month-old Thai female newborn with multiple hypopigmented flat-topped papules without any internal organ involvement including normal blood cell c...
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ورودعنوان ژورنال:
- Acta dermatovenerologica Alpina, Pannonica, et Adriatica
دوره 17 4 شماره
صفحات -
تاریخ انتشار 2008